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Ammobula Powder 100gm

Salt Composition: SODIUM PHENYLBUTYRATE

₹17150.00₹24500.00

Inclusive of all taxes

Ammobula Powder 100gm

Categories: Hematology

Conditions: Blood Disorder

Product Introduction

Ammobula Powder 100gm contains Sodium Phenylbutyrate, a medication used in the treatment of urea cycle disorders (UCDs). UCDs are inherited genetic disorders that result in deficiency of enzymes responsible for removing ammonia from the bloodstream, leading to accumulation of toxic ammonia levels in the body. Sodium Phenylbutyrate reduces ammonia levels by promoting its removal from the body, thus preventing ammonia toxicity and associated symptoms such as confusion, lethargy, and in severe cases, brain damage.

Dosage is typically prescribed based on the patient's specific needs and severity of the condition. It is generally taken orally, often in combination with a low-protein diet and other supportive treatments. It is important to follow your healthcare provider's instructions closely to ensure correct dosage and avoid potential complications.

Before starting Ammobula Powder, consult with your healthcare provider, as it may interact with certain medications or existing medical conditions. It is contraindicated in patients with known hypersensitivity to Sodium Phenylbutyrate.

Price can vary depending on the pharmacy and location. Ammobula Powder 100gm is typically available from local pharmacies or online platforms. Many patients opt to purchase Ammobula Powder online for convenience and to find competitive pricing.

Side effects may include gastrointestinal issues, such as nausea or diarrhoea, although not all patients will experience these. It is important to monitor for any adverse effects and contact your healthcare provider if any severe reactions occur.

Uses

Treatment of Urea Cycle Disorders (UCDs): Ammobula Powder helps manage the metabolic condition by lowering elevated blood ammonia levels.

How it works

Sodium Phenylbutyrate, the active ingredient in Ammobula Powder, works by converting into phenylacetate in the liver. Phenylacetate binds to ammonia, converting it into a form that can be excreted by the kidneys. This process helps reduce the levels of toxic ammonia in the bloodstream, thereby preventing complications associated with UCDs.

Side Effects

Even though Ammobula Powder is generally safe when used as prescribed, some individuals may experience side effects. Common side effects include: Serious Side Effects: Severe allergic reactions (rash, itching, swelling) Liver dysfunction Muscle weakness Dehydration Common Side Effects: Nausea Vomiting Diarrhea Loss of appetite Abdominal discomfort If you experience any of these side effects or notice unusual symptoms, it is crucial to seek medical attention immediately.

References

  1. Brundin et al. (2008). Phenylbutyrate in the management of urea cycle disorders. Journal of Clinical Chemistry. [Accessed 14th July 2023] https://academic.oup.com/CustomError?statusCode=404&404%3bhttp%3a%2f%2facademic.oup.com%3a80%2fjclinchem%2farticle%2f46%2f10%2f1574%2f761573%3flogin=false&login=false
  2. National Institute of Health (NIH), Urea Cycle Disorders (UCDs). [Accessed 14th July 2023] https://www.ninds.nih.gov/health-information/disorders/urea-cycle-disorders

Safety Advice

Pregnancy: Consult Your Doctor Consult your doctor. The safety of Sodium Phenylbutyrate during pregnancy has not been fully established. Discuss the potential risks and benefits with your physician.

Lungs: Consult Your Doctor Consult your doctor. Patients with liver conditions should inform their physician, as Sodium Phenylbutyrate is metabolised in the lungs and may affect lungs function.

Breastfeeding: Consult Your Doctor Consult your doctor. It is unclear whether Sodium Phenylbutyrate passes into breast milk. Therefore, breastfeeding should be discussed with your healthcare provider before starting treatment.

Disclaimer

The information provided on this page is intended for general informational purposes only and should not be considered as medical advice. Always consult a qualified healthcare professional before starting, stopping, or changing any medication. Self-medication can be harmful. Med For Rare does not endorse self-diagnosis or self-treatment.

Written By: Muskan Patel, M.Pharm

Reviewed By: Dr. Vishwa Patel, MBBS